Scimitar Sendromu:  Olgu Sunumu

Aksoy, Emine; Tokyay, Dilem An�l; Tokg�z Aky�l, Fatma; K�l��, Ay�e �rem; Sevim, T�lin

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Laparoscopic Endoscopic Surgical Science Scimitar Sendromu: Olgu Sunumu [Respir Case Rep]

Respir Case Rep. 2015; 4(3): 200-203 | DOI: 10.5505/respircase.2015.58070

Scimitar Sendromu: Olgu Sunumu

Emine Aksoy, Dilem An�l Tokyay, Fatma Tokg�z Aky�l, Ay�e �rem K�l��, T�lin Sevim
S�reyyapa�a G��s Hastal�klar� ve G��s Cerrahisi E�itim ve Ara�t�rma Hastanesi, G��s Hastal�klar� Klini�i, �stanbul

Scimitar sendromu veya pulmoner venolober sendrom, nadir g�r�len bir konjenital ven�z d�n�� anomalisidir. K�rk yedi ya��nda kad�n hasta, g��s a�r�s� ve eforla geli�en nefes darl�� ik�yeti ile ba�vurdu. Fizik muayenesi ve laboratuvar bulgular� normaldi. Postero-anterior akci�er grafisinde sa� akci�er alt alanda sa� kalp kenar� boyunca nonhomojen opasite art��, sa� akci�erde vol�m kayb�, kalp g�lgesinin sa�a do�ru yer de�i�tirdi�i izlendi. Ekokardiyografide sistolik pulmoner arter bas�nc� 55 mmHg �l��ld�. Fiberoptik bronkoskopide sa� bron�ial sistemde ara bron�un olmad�� g�r�ld�. Manyetik rezonans anjiografide, Scimitar sendromu ile uyumlu olarak sa� pulmoner venlerin subdiafragmatik mesafede inferior vena kavaya drene oldu�u izlendi. Anormal pulmoner ven�z d�n��, sa� akci�er hipoplazisi, ara bron� anomalisi ve pulmoner hipertansiyon ile Scimitar sendromu tan�s� konulan olgumuz literat�rler e�li�inde sunuldu.

Anahtar Kelimeler: Pulmoner hipertansiyon, pulmoner ven, scimitar sendromu.

Scimitar Syndrome: A Case Report

Emine Aksoy, Dilem An�l Tokyay, Fatma Tokg�z Aky�l, Ay�e �rem K�l��, T�lin Sevim
Department of Chest Diseases, S�reyyapa�a Chest Diseases and Thoracic Surgery Training and Research Hospital, �stanbul, Turkey

Scimitar syndrome or pulmonary venolabar syndrome is a rare congenital anomalous pulmonary venous return. A 47-year-old woman presented at our clinic with chest pain and shortness of breath during exertion. The physical examination and laboratory findings were normal. The chest radiograph demonstra-ted non-homogeneous increased opacity along the right cardiac border, and volume loss of the right lung with cardiac silhouette displacement, to the right. Echocardiography pulmonary artery systolic pressure was measured as 55 mmHg. Fiberoptic bronchoscopy revealed the intermediate bronchus was absent. On magnetic resonance angiography, it was observed that the right pulmonary veins drained into the inferior vena cava at a subdiaphragmatic level, consistent with Scimitar Syndrome. The case, diagnosed as Scimitar syndrome, is presented in the light of the literature.

Keywords: Pulmonary hypertension, pulmonary vein, scimitar syndrome.

Sorumlu Yazar: Dilem An�l Tokyay, T�rkiye
Makale Dili: T�rk�e

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