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Pulmoner Langerhans Hcreli Histiositozis X: Drt olgunun analizi [Respir Case Rep]
Respir Case Rep. 2013; 2(3): 106-111 | DOI: 10.5505/respircase.2013.70298

Pulmoner Langerhans Hcreli Histiositozis X: Drt olgunun analizi

Pnar Yldz Glhan, Aydanur Ekici, Emel Bulcun, Mehmet Sava Ekici
Krkkale Universitesi Tp Fakltesi Gs Hastalklar Ana Bilim Dal, Krkkale

Pulmoner langerhans hcreli histiositozis (PLHH) X langerhans hcreli histiositozisin alt grubu olup akcierlerde langerhans hcre infiltrasyonunun grld nedeni bilinmeyen bir interstisiyel akcier hastaldr. Klinik spektrumu non-prodktif ksrk, nefes darlndan spontan pnmotoraksa kadar ok geni olup olgularn % 90'ndan fazlas sigara iicisidir. Yksek znrlkl bilgisayar tomografide (YBT) st ve orta zonlarda retiklonodler ve kistik grnmlerin olmas karakteristiktir. PLHH nadir grlen bir hastalktr, gen, sigara ien ve spontan pnmotoraks nedeniyle bavuran hastalarda akla gelmelidir. Nadir grlen bir hastalk olmas nedeniyle takip ettiimiz 4 olguyu literatre katmak amacyla sunduk.

Anahtar Kelimeler: histiositozis X, sigara, spontan pnmotoraks

Pulmonary Langerhans cell histiocytosis X: an analysis of four cases

Pnar Yldz Glhan, Aydanur Ekici, Emel Bulcun, Mehmet Sava Ekici
Department of Pulmonary Medicine, University of Kirikkale, Faculty of Medicine, Kirikkale,

Pulmonary Langerhans Cell Histiocytosis (PLCH) X, which is a subgroup of Langerhans Cell Histioycytosis, is an idiopathic interstitial lung disease in which Langerhans cell infiltration is seen in the lung. PLCH X has a wide spectrum of symptoms from nonproductive cough and dyspnea to spontaneous pneumothorax, and more than 90 % patients who have these diseases are smokers. Reticular and cystic patterns were observed on the upper and middle lung lobes at high resolution computed tomography. PLCH X is a rare disease, and should be considered in patients who are younger, smokers, and patients who apply to the hospital by presenting with spontaneous pneumothorax. To contribute to the literature, four cases, which were followed, are presented, as it is a rare disease.

Keywords: histiocytosis X, cigarettes, spontaneous pneumothorax

Pnar Yldz Glhan, Aydanur Ekici, Emel Bulcun, Mehmet Sava Ekici. Pulmonary Langerhans cell histiocytosis X: an analysis of four cases. Respir Case Rep. 2013; 2(3): 106-111

Sorumlu Yazar: Pnar Yldz Glhan, Trkiye
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