Pulmonary Tuberculosis in a Patient with Marfan's Syndrome with Pulmonary Involvement

Marfan's syndrome (MFS) is a connective tissue disorder inherited by autosomal dominance and primarily affecting the ocular, musculoskeletal, and cardiovascular systems. Its pulmonary manifestations, such as spontaneous pneumothorax, apical blebs, and bullae, are rarely seen. We present a young male patient, incidentally diagnosed with MFS, while under treatment for chronic pulmonary tuberculosis. Apical parenchymal involvement of MFS and pulmonary tuberculosis were discussed.

Marfan Sendromu Akciðer Tutulumu Bulunan Olguda Akciðer Tüberkülozu

Marfan sendromu (MFS) otozomal dominant geçiþ gösteren öncelikle oküler, kas-iskelet ve kardiyovasküler sistemleri tutan bir bað dokusu hastalýðýdýr. Hastalýðýn; spontan pnömotoraks, apikal bül veya blebler gibi akciðer belirtileriyle nadiren karþýlaþýlýr. Bu sunumda kronik akciðer tüberkülozu tedavisi altýnda iken rastlantýsal olarak MFS tanýsý konulan genç bir erkek hasta sunuldu. MFS’nin apikal parankim tutulumu ve akciðer tüberkülozu tartýþýldý.