Respir Case Rep. 2021; 10(1): 59-62 | DOI: 10.5505/respircase.2021.04696

Malignant Peripheral Nerve Sheath Tumor Related to Diffuse Neurofibroma of Chest Wall

Muharrem Çakmak¹, Ýsmail Demirel^2
1Fýrat University Faculty of Medicine, Department of Thoracic Surgery, Elazig, Turkey.
²Fýrat University Faculty of Medicine, Department of Anesthesiology and Reanimation, Elazig, Turkey.

Malignant peripheral nerve sheath tumors account for 5–10% of all soft tissue tumors. These tumors are closely related with Neurofibromatosis type 1. Although many such tumors have been reported in different locations, malignant peripheral nerve sheath tumors arising from diffuse neurofibroma located in the chest wall are extremely rare. In the present study we report on a malignant peripheral nerve sheath tumor arising out of a diffuse neurofibroma of the chest wall.

Keywords: Chest wall, Mass, Malignant peripheral nerve sheath tumor

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Göðüs Duvarýnýn Diffüz Nörofibroma ile Ýliþkili Malign Periferal Sinir Kýlýfý Tümörü

Muharrem Çakmak¹, Ýsmail Demirel^2
1Fýrat Üniversitesi Týp Fakültesi, Göðüs Cerrahisi Anabilim Dalý, Elazýð, Türkiye
²Fýrat Üniversitesi Týp Fakültesi, Anesteziyoloji ve Reanimasyon Anabilim Dalý, Elazýð, Türkiye

Malign periferik sinir kýlýfý tümörü yumuþak doku tümörlerinin %5-10’unu oluþturur. Bu tümörler Nörofibromatozis tip 1 ile yakýndan iliþkilidir. Farklý lokalizasyonlarda birçok olgu bildirilmiþ olsa da göðüs duvarý yerleþimli diffüz nörofibroma zemininde geliþen malign periferik sinir kýlýfý tümörü son derece nadirdir. Bu çalýþmada, göðüs duvarý yerleþimli diffüz nörofibroma zemininde geliþen malign periferik sinir kýlýfý tümörünü sunuyoruz.

Anahtar Kelimeler: Göðüs duvarý, Kitle, Malign periferik sinir kýlýfý tümörü

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