Respir Case Rep. 2016; 5(3): 161-164 | DOI: 10.5505/respircase.2016.36854

Pulmonary Alveolar Proteinosis and Tracheal Stenosis After Exposure to Fire and Fire Extinghuisher

Mustafa Çörtük¹, Elif Tanrýverdi O², Kenan Abbaslý², Mehmet Akif Özgül², Erdoðan Çetinkaya^2
1Department of Chest Diseases, Karabük University Faculty of Medicine. Karabük, Turkey
²Department of Chest Diseases, Yedikule Chest Diseases and Thoracic Surgery Training and Research Hospital. Ýstanbul, Turkey

Pulmonary alveolar proteinosis (PAP) is a rare disease characterized by the accumulation of acellular surfactant lipids and proteins within the alveoli. Idiopathic PAP accounts for about 90% of all patients. Secondary PAP factors include insecticides, inorganic dusts such as silica, hematological malignancies, Human Immunodeficiency Virus infection, leflunomide, toxic gas inhalation, various industrial exposures to aluminum- and metal oxide-containing dusts and clinical conditions. Herein, we present a case of pulmonary alveolar proteinosis and tracheal stenosis secondary to exposure to fire and fire extinguisher.

Keywords: Pulmonary Alveolar Proteinosis, Fire extinguishing systems, Smoke Inhalation Injury

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Yangýn ve Yangýn Söndürücü Maruziyeti Sonrasýnda Geliþen Pulmoner Alveolar Proteinozis ve Trakeal Stenoz

Mustafa Çörtük¹, Elif Tanrýverdi O², Kenan Abbaslý², Mehmet Akif Özgül², Erdoðan Çetinkaya^2
1Karabük Üniversitesi Týp Fakültesi, Göðüs Hastalýklarý Ana Bilim Dalý, Karabük
²Yedikule Göðüs Hastalýklarý ve Göðüs Cerrahisi Eðitim ve Araþtýrma Hastanesi, Göðüs Hastalýklarý Kliniði, Ýstanbul

Pulmoner alveoler proteinozis (PAP) nadir bir hastalýktýr. PAP alveollere aselüler sürfaktan lipidlerin ve proteinlerin birkimi ile karakterizedir. Ýdiyopatik PAP bütün PAP olgularýnýn %90’ýný oluþturur. Sekonder PAP ise insektisitlerle, silika gibi inorganik tozlara, hematolojik malignitelere, insan immün yetmezlik virüs infeksiyonuna, leflunomide, toksik gaz inhalasyonuna, alüminyum ve metal oksit içeren endüstriyel tozlara sekonder geliþebilir. Biz de yangýn ve yangýn söndürücü maruziyeti sonrasý geliþen pulmoner alveolar proteinozis ve trakeal stenoz olgusu sunduk.

Anahtar Kelimeler: Pulmoner alveoler proteinoz, Yangýn söndürme sistemleri, Duman inhalasyon hasarý

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