Respir Case Rep. 2021; 10(3): 180-185 | DOI: 10.5505/respircase.2021.38039

Hemangiolymphangioma with Accompanying Interstitial Lung Disease: A Rare Case

Gülçehre Oðuztürk¹, Selin Onay Mahmuti², Ece Yasemin Demirkol², Neslihan Fener³, Ekrem Cengiz Seyhan¹, Erdoðan Çetýnkaya¹, Muzaffer Metin^2
1Department of Chest Diseases, Health Science University, Yedikule Training and Research Hospital for Chest Diseases and Thoracic Surgery, Ýstanbul, Turkey
²Department of Thoracic Surgery, Health Science Uni-versity, Yedikule Training and Research Hospital for Chest Diseases and Thoracic Surgery, Ýstanbul, Turkey
³Department of Pathology, Health Science University, Yedikule Training and Research Hospital for Chest Diseases and Thoracic Surgery, Ýstanbul, Turkey

Vascular anomalies are pathologies that occur in embryonic life that affect the lymphatic and capillary systems, and can be classified as vascular tumors or vascular malformations, according to their histological features. They are rare and are mostly detected in the first years of life. Hemangio-lymphangiomas are benign vascular tumors containing lymphatic and capillary system elements with a reported incidence of 1: 12,000 in newborns. The cases reported to date have been in the head (oral cavity, orbita, etc.), neck and mediastinum regions. We presented here a case of a 17-year-old male patient who was diagnosed with hemangiolymphangioma after a videoassisted lung biopsy (VATS) with accompa-nying interstitial lung disease. The patient, who had no history of chronic disease, pre-sented to the outpatient clinic complaining of cough and shortness of breath for eight months. Interstitial lung features were ob-served in the patient’s thorax computer tomography. After the VATS procedure, the patient developed chylothorax, and the pathology results indicated hemangiolymphangioma.

Keywords: Hemangiolymphangioma, chylothorax, interstitial, lung.

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Ýnterstistiyel Akciðer Hastalýðý ile Seyreden Hemanjiyolenfanjioma: Nadir Bir Olgu

Gülçehre Oðuztürk¹, Selin Onay Mahmuti², Ece Yasemin Demirkol², Neslihan Fener³, Ekrem Cengiz Seyhan¹, Erdoðan Çetýnkaya¹, Muzaffer Metin^2
1SBÜ Yedikule Göðüs Hastalýklarý ve Göðüs Cerrahisi Eðitim ve Araþtýrma Hastanesi, Göðüs Hastalýklarý Kliniði, Ýstanbul
²SBÜ Yedikule Göðüs Hastalýklarý ve Göðüs Cerrahisi Eðitim ve Araþtýrma Hastanesi, Göðüs Cerrahisi Kliniði, Ýstanbul
³SBÜ Yedikule Göðüs Hastalýklarý ve Göðüs Cerrahisi Eðitim ve Araþtýrma Hastanesi, Patoloji Kliniði, Ýstanbul

Vasküler anomaliler, embriyonik yaþamda oluþan, lenfatik ve kapiller sistemleri etkileyen patolojilerdir ve histolojik özelliklerine göre vasküler tümörler veya vasküler malformasyonlar olarak sýnýflandýrýlýrlar. Nadir görülürler ve daha çok yaþamýn ilk yýllarýnda saptanýrlar. Hemanjiyolenfanjiyomlar da lenfatik ve kapiller sistem elemanlarý içeren, benign bir vasküler tümördür. Ýnsidansý yenidoðanlarda 1/12.000 olarak bildirilmiþtir. Bugüne dek bildirilen olgular baþ bölgesi (aðýz boþluðu, orbita vs), boyun ve mediasten bölgelerindedir. Biz de bu makalede interstistiyel akciðer hastalýðý ile seyreden ve yapýlan tanýsal video yardýmlý akciðer bi-yopsisi (VATS) iþlemi sonrasýnda hemanjiyolenfanjiyoma tanýsý alan 17 yaþýnda bir erkek hastayý sunduk. Kronik bir hastalýðý olmayan ve sekiz aydýr olan öksürük ve nefes darlýðý ile polikliniðe baþvuran hastaya çekilen toraks tomografisinde interstistiyel akciðer özellikleri görülmüþ olup; VATS iþlemi sonra-sýnda hastada þilotoraks geliþti. Patoloji so-nucu hemanjiyolenfanjiyom olarak sonuçlandý.

Anahtar Kelimeler: Hemanjiyolenfanjiyom, þilotoraks, interstistiyel, akciðer.

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