Hybrid Congenital Lung Malformation with Difficulty in Diagnosis and Treatment: Congenital Cystic Adenoid Malformation and Pulmonary Sequestration Co-existence

Congenital abnormalities of the lung can manifest in any component of the bronchopulmonary system. Congenital lobar emphysema, bronchogenic cyst, congenital cystic adenoid malformation (CCAM) or pulmonary sequestration (PS) are just some of the many kinds of malformations of the lung. The co-existence of CCAM and PS is a very rare condition. Due to such complications as dyspnea or recurrent infection, most malformations are diagnosed antenatally or in the immediate postnatal period. The present case was not diagnosed until late adolescence, and the patient was subsequently referred to our clinic after undergoing a previous operation. After examinations and a preoperative evaluation, a second operation was performed. We present to literature a very rare case of co-existing CCAM and PS (hybrid lung malformation).

Taný veTedavide Zorluk Yaþatan Hibrid Konjenital Akciðer Malformasyonu: Konjenital Kistik Adenoid Malformasyon ve Pulmoner Sekestrasyon Birlikteliði

Akciðerin konjenital anomalileri bronkopulmoner sistemin tüm bileþenlerinden kaynaklanabilir. Konjenital lober amfizem, bronkojenik kist, konjenital kistik adenoid malformasyon (KKAM) veya pulmoner sekestrasyon (PS) bronkopulmoner malformasyonlardýr. KKAM ve PS birlikte çok nadir görülmektedir. Solunum sýkýntýsý, tekrarlayan enfeksiyonlar gibi komplikasyonlar nedeniyle çoðu antenatal veya postnatal dönemde taný almaktadýr. Eriþkin yaþa kadar taný ve tedavisinde sorunlar yaþanan bir olgu, ileri taný ve tedavi amaçlý kliniðimize yönlendirildi. Tetkik ve deðerlendirmeler sonrasýnda kliniðimizde ikinci kez operasyon yapýldý. Çok nadir görülen KKAM ve PS birlikteliði (hibrid konjenital malformasyon) saptanan olguyu literatür eþliðinde sunmayý amaçladýk.

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