Respir Case Rep. 2018; 7(3): 169-172 | DOI: 10.5505/respircase.2018.33154

Congenital Lobar Emphysema: Report of Two Cases

Fatih Meteroðlu¹, Atalay Þahin², Menduh Oruç^1
1Dicle University, Medical School, Department of Thoracic Surgery, Diyarbaki, Turkey
²Harran University, Medical School, Department of Thoracic Surgery, Sanlýurfa\ Turkey

Congenital lobar emphysema is a cause of respiratory distress characterized by hyperexpansion of 1 or more lobes of the lung, compression onto the ipsilateral or contralateral functional pulmonary parenchymas, and a resultant mediastinal shift. The onset of symptoms may be delayed until the age of 6 months, although the disease causes dyspnea in newborns or infancy. It is a rarely seen disease. Awareness is important due to confusion with pneumothorax and the possibility of considerable clinical improvement with early surgical intervention, even in severe cases. Two male patients with failed conservative treatment, 4 and 27 months of age, were hospitalized in this clinic because of respiratory distress and repeated infections. A left upper lobectomy was performed due to lobar emphysema in both patients. The goal of this report was to present the improvement in respiratory function and general condition of 2 patients observed after surgical management.

Keywords: congenital lobar emphysema, lobectomy, dyspnea

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Konjenital Lober Amfizem: Ýki Olgu Sunumu

Fatih Meteroðlu¹, Atalay Þahin², Menduh Oruç^1
1Dicle Üniversitesi Týp Fakültesi Göðüs Cerrahisi AD\ Diyarbakir
²Harran Üniversitesi Týp Fakültesi Göðüs Cerrahisi AD\ Þanlýurfa

Konjenital lober amfizem; akciðerin bir veya daha fazla lobunun hiperekspansiyonu, bunun çevredeki normal akciðer dokusuna basýsý ve mediastinal kayma ile karakterli bir respiratuvar distres nedenidir. Yeni doðan döneminde solunum sýkýntýsýna yol açmakla birlikte, ender olarak semptomlarýn ortaya çýkýþý altýncý aya kadar gecikebilir. Nadir görülen bir hastalýktýr. Spontan pnömotoraks ile karýþtýrýlmasý ve ciddi olgularda uygulanan acil cerrahi müdahale ile klinik tablonun dramatik olarak düzelmesi nedeniyle önem taþýmaktadýr. Kliniðimizde solunum sýkýntýsý, sýk sýk enfeksiyon nedeniyle medikal tedavi alan 4 ve 27 aylýk iki erkek olgu yatýrýldý. Her iki olguya da lober amfizem nedeniyle sol üst lobektomi yapýldý. Cerrahi iþlem sonrasý takiplerinde genel durumlarýnda ve solunum düzeylerinde ciddi düzelmeler olan iki olguyu sunmayý amaçladýk.

Anahtar Kelimeler: konjenital lober amfizem, lobektomi, solunum sýkýntýsý.

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