Pulmonary Langerhans cell histiocytosis X: an analysis of four cases

Pulmonary Langerhans Cell Histiocytosis (PLCH) X, which is a subgroup of Langerhans Cell Histioycytosis, is an idiopathic interstitial lung disease in which Langerhans cell infiltration is seen in the lung. PLCH X has a wide spectrum of symptoms from nonproductive cough and dyspnea to spontaneous pneumothorax, and more than 90 % patients who have these diseases are smokers. Reticular and cystic patterns were observed on the upper and middle lung lobes at high resolution computed tomography. PLCH X is a rare disease, and should be considered in patients who are younger, smokers, and patients who apply to the hospital by presenting with spontaneous pneumothorax. To contribute to the literature, four cases, which were followed, are presented, as it is a rare disease.

Pulmoner Langerhans Hücreli Histiositozis X: Dört olgunun analizi

Pulmoner langerhans hücreli histiositozis (PLHH) X langerhans hücreli histiositozisin alt grubu olup akciðerlerde langerhans hücre infiltrasyonunun görüldüðü nedeni bilinmeyen bir interstisiyel akciðer hastalýðýdýr. Klinik spektrumu non-prodüktif öksürük, nefes darlýðýndan spontan pnömotoraksa kadar çok geniþ olup olgularýn % 90'ýndan fazlasý sigara içicisidir. Yüksek çözünürlüklü bilgisayar tomografide (YÇBT) üst ve orta zonlarda retikülonodüler ve kistik görünümlerin olmasý karakteristiktir. PLHH nadir görülen bir hastalýktýr, genç, sigara içen ve spontan pnömotoraks nedeniyle baþvuran hastalarda akla gelmelidir. Nadir görülen bir hastalýk olmasý nedeniyle takip ettiðimiz 4 olguyu literatüre katmak amacýyla sunduk.