Respir Case Rep. 2017; 6(3): 166-169 | DOI: 10.5505/respircase.2017.98698

Primary Pulmonary Extranodal Marginal Zone Lymphoma: An Atypical Radiological Pattern

Pýnar Akýn Kabalak¹, Miraç Öz¹, Duygu Kankaya², Aydýn Çiledað¹, Çetin Atatsoy³, Muhit Özcan⁴, Özlem Özdemir Kumbasar^1
1Department Of Chest Disease, Ankara University, Faculty of Medicine, Ankara, Turkey
²Department Of Pathology, Ankara University, Faculty of Medicine, Ankara, Turkey
³Department Of Radiology, Ankara University, Faculty of Medicine, Ankara, Turkey
⁴Department Of Hematology, Ankara University, Faculty of Medicine, Ankara, Turkey

Primary pulmonary extranodal marginal zone lymphoma (PPEMZL) arising from the mucosa-associated lymphoid tissue of the bronchus is a very rare disorder. It appears in the form of a slowly progressing localized mass or consolidation. Clinical presentation may include non-specific pulmonary symptoms, such as chronic cough, or dyspnea, but it is more often diagnosed incidentally. Computed tomography (CT) the thorax revealed that the present patient had a giant cystic lesion, parenchymal nodules, and consolidation area. The patient was symptomatic and diagnosed as marginal zone lymphoma by immunohistochemical study of the transthoracic biopsy specimen. This patient is thought to be the first diagnosed as PPEMZL from a cystic lesion.

Keywords: Cystic lesion, immunohistochemical staining, pulmonary lymphoma, marginal zone

---

Primer Pulmoner Ekstranodal Marjinal Zon Lenfoma: Atipik Radyolojik Görünüm

Pýnar Akýn Kabalak¹, Miraç Öz¹, Duygu Kankaya², Aydýn Çiledað¹, Çetin Atatsoy³, Muhit Özcan⁴, Özlem Özdemir Kumbasar^1
1Ankara Üniversitesi Týp Fakültesi, Göðüs Hastalýklarý Ana Bilim Dalý, Ankara
²Ankara Üniversitesi Týp Fakültesi, Patoloji Ana Bilim Dalý, Ankara
³Ankara Üniversitesi Týp Fakültesi, Radyoloji Ana Bilim Dalý, Ankara
⁴Ankara Üniversitesi Týp Fakültesi, Hematoloji Ana Bilim Dalý, Ankara

Bronþa ait mukoza iliþkili lenfoid dokudan kaynaklanan primer pulmoner ekstranodal marjinal zon lenfoma nadir görülmektedir. Yavaþ progrese olan lokalize kitle ya da konsolidasyon olarak ortaya çýkar. Kronik öksürük, dispne gibi non-spesifik pulmoner semptomlar olabilir ama sýklýkla tesadüfen taný alýr. Hastamýza ait toraks tomografisinde dev kistik bir lezyon ve eþlik eden konsolidasyon ve nodüller vardý. Transtorasik akciðer biopsisi ve immünhistokimayasal inceleme ile marjinal zon lenfoma tanýsý elde edildi. Dev kistik lezyon ile radyolojik bulgu veren ilk olgu olarak sunmayý amaçladýk.

Anahtar Kelimeler: Kistik lezyon, immünhistokimyasal boyama, pulmoner lenfoma, marjinal zon

---

Image Slices of the Case

---

CITE