Respir Case Rep. 2017; 6(3): 174-176 | DOI: 10.5505/respircase.2017.59023

Poland Sendromu: Ýki Olgu Sunumu

Tayfun Kermenli¹, Adil Doðan^2
1Elbistan Devlet Hastanesi, Göðüs Cerrahisi Kliniði, Kahramanmaraþ
²Elbistan Devlet Hastanesi, Radyoloji Birimi, Kahramanmaraþ

Poland sendromu pektoralis majör kasýnýn yokluðu ile karakterize konjenital bir sendromdur.Bu sendrom ile beraber, ayný tarafta pektoralis minör kasýnýn yokluðu, göðüs ve üst ekstremite deformiteleri, meme dokusunun geliþmemesi, aksillada alopesi, 2. ila 5. arasýndaki kaburgalarýn olmamasý, latissimus dorsi, serratus anterior ve eksternal oblik kaslarýnýn geliþmemiþ olmasý gibi ilave bulgular görülebilir. Ayný taraflý toraks çöküklüðü, toraksta paradoksal hareket ve akciðer herniasyonu da bulunabilir. Poland sendromunun genel olarak 1/30000 sýklýkta görüldüðü tahmin edilmektedir. Eriþkin yaþta taný konulmasý nedeniyle bu iki nadir olguyu sunuyoruz.

Anahtar Kelimeler: Poland sendromu, konjenital toraks anomalisi, pektoral kas

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Poland Syndrome: A Report of Two Cases

Tayfun Kermenli¹, Adil Doðan^2
1Department of Thoracic Surgery, Elbistan State Hospital, Kahramanmaraþ, Turkey
²Department of Radiology, Elbistan State Hospital, Kahramanmaraþ, Turkey

Poland syndrome is a congenital syndrome characterized by the absence of the pectoralis major muscle. Additional findings may include a lack of the pectoralis minor muscle, breast and upper extremity deformities, nondevelopment of breast tissue, axillary alopecia, and the absence of ribs 2 to 5, the latissimus dorsi, serratus anterior, and the external oblique muscles. Same side thoracic depression, paradoxical movement of the thorax and pulmonary hernia may occur. It is estimated that Poland syndrome is generally seen at a frequency of 1/30000. Presently described are these 2 cases that are rare due to diagnosis at adult age.

Keywords: Poland syndrome, congenital thorax anomaly, pectoral muscle

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Olgunun Görüntü Kesitleri

Ýkinci Olgu

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ATIF KOPYALA