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Primer Pulmoner Leiomiyosarkom [Respir Case Rep]
Respir Case Rep. 2013; 2(1): 35-38 | DOI: 10.5505/respircase.2013.35744

Primer Pulmoner Leiomiyosarkom

Nurdan Þimþek Veske1, Gülþah Günlüoðlu1, Adalet Demir2, Pelin Karadað1, Ekrem Cengiz Seyhan1, Nur Ürer3, Sedat Altýn1
1Yedikule Göðüs Hastalýklarý Ve Göðüs Cerrahisi Eðitim Ve Araþtýrma Hastanesi, Göðüs Hastalýklarý Kliniði, Ýstanbul
2Yedikule Göðüs Hastalýklarý Ve Göðüs Cerrahisi Eðitim Ve Araþtýrma Hastanesi, Göðüs Cerrahisi Kliniði
3Yedikule Göðüs Hastalýklarý Ve Göðüs Cerrahisi Eðitim Ve Araþtýrma Hastanesi, Patoloji Bölümü, Ýstanbul

Leiomiyosarkom, sýklýkla uterus, retroperitoneum ve intraabdominal bölgeden kaynaklanan, düz has hücrelerinin tümörüdür. Trakeabronþiyal aðaçta düz kas hücrelerinin çokluðuna raðmen primer pulmoner kas tümörleri çok nadirdir. Kýrk sekiz yaþýnda herhangi bir þikayeti olmayan erkek hasta, tesadüfen çekilen akciðer grafisinde lezyon saptanmasý nedeniyle merkezimize yönlendirilmiþti. Bilgisayarlý Toraks tomografisinde sað akciðer alt lobda 4x3 cm çaplý kitlesel lezyon izlendi. Fluorodeoksiglukoz (FDG) iþaretli Bilgisayarlý Tomografi Entegrasyonlu Positron Emisyon Tomografi (PET/CT) taramada lezyonun düþük FDG tutulumu mevcuttu. Tanýsal amaçlý tomografi rehberliðinde iðne aspirasyonlarý yapýldý. Histopatolojik tanýya ulaþýlamayýnca taný ve tedavi amacýyla cerrahi planlandý. Video yardýmlý toraks cerrahisi (VATS) ile alt lob wedge rezeksiyonu uygulanan hastanýn postoperatif patoloji sonucu akciðerin primer leiomiyosarkomu olarak yorumlandý.

Anahtar Kelimeler: Pulmoner sarkom, leiomiyosarkom, PET/CT.

Primary Pulmonary Leiomyosarcoma

Nurdan Þimþek Veske1, Gülþah Günlüoðlu1, Adalet Demir2, Pelin Karadað1, Ekrem Cengiz Seyhan1, Nur Ürer3, Sedat Altýn1
1Yedikule Chest Diseases And Thoracic Surgery Education And Research Hospital, Departman Of Chest Diseases, Ýstanbul
2Yedikule Chest Diseases And Thoracic Surgery Education And Research Hospital, Departman Of Thoracic Surgery, Ýstanbul
3Yedikule Chest Diseases And Thoracic Surgery Education And Research Hospital, Departman Of Pathology, Ýstanbul

Leiomyosarcoma is a tumor of the smooth muscle cells which frequently originates in the uterus, retro-peritoneum, and within the abdomen. Although there are a large number of smooth muscle cells in the tracheobronchial tree, primary pulmonary muscle tumors rarely occur. A 48-year-old male patient with no symptoms was admitted to our department following the inadvertent detection of a lesion in his chest x-ray. Through thoracic computerized tomography, a 4x3 cm diameter mass lesion was located in the lower right lobe. In the positron emission tomography-computed tomography (PET/CT) scan with a fluorodeoxyglucose (FDG) tracer, low FDG uptake was observed in the lesion. Computer tomography-guided needle aspirations were carried out. In the absence of a histopathological diagnosis, surgery was planned for diagnosis and treatment. A lower lobe wedge resection was completed using video-assisted thoracic surgery (VATS). A diagnosis of primary pulmonary leiomyosarcoma was made based on postoperative pathology results.

Keywords: Pulmonary sarcoma, leiomyosarcoma, PET/CT.

Nurdan Þimþek Veske, Gülþah Günlüoðlu, Adalet Demir, Pelin Karadað, Ekrem Cengiz Seyhan, Nur Ürer, Sedat Altýn. Primary Pulmonary Leiomyosarcoma. Respir Case Rep. 2013; 2(1): 35-38

Sorumlu Yazar: Nurdan Þimþek Veske, Türkiye
Makale Dili: Türkçe
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