e-ISSN 2147-2475
Cilt : 6 Say : 2 Yl : 2022

Hzl Arama




Laparoscopic Endoscopic Surgical Science Yeni bir tanm: Kombine pulmoner fibrozis ve amfizem sendromu [Respir Case Rep]
Respir Case Rep. 2017; 6(2): 110-113 | DOI: 10.5505/respircase.2017.93585

Yeni bir tanm: Kombine pulmoner fibrozis ve amfizem sendromu

Dildar Duman, Hakan Gnen
Sreyyapaa Gs Hastalklar ve Gs Cerrahisi Eitim Aratrma Hastanesi, stanbul

Kombine pulmoner fibrozis ve amfizem sendromu (KPFA), kendine zg klinik bulgular olan ve radyolojik olarak st lob amfizemi ve alt lob fibrozisi ile karakterize yeni tanmlanan bir sendromdur. Hastalk iyi bilinmedii iin yeterince tan konulamamaktadr. Progresif nefes darl ikayetiyle bavuran, 60 paket/yl sigara yks olan erkek hastann ekilen toraks tomografisinde KPFA sendromuna zg st loblarda amfizem ve alt loblarda fibrozis izlendi. Hastaln bir dier nemli zelii olarak FEV1 ksmen korunmu, DLCO ise olduka dk bulundu. hastada pulmoner hipertansiyon saptand. Tm bulgularyla KPFA sendromu tans konulan olgu, bu sendromuna dikkat ekmek iin literatr eliinde sunuldu.

Anahtar Kelimeler: amfizem, fibrozis, pulmoner hipertansiyon

A new definition: Combined pulmonary fibrosis and emphysema syndrome

Dildar Duman, Hakan Gnen
Sreyyapaa Chest Diseases and Thoracic Surgery Trainig and Research Hospital, Istanbul, Turkey

Combined pulmonary fibrosis and emphysema syndrome (CPFE) is a newly defined syndrome with unique clinical findings, characterized by presence of emphysema and pulmonary fibrosis seen radiologically. Since awareness of the syndrome is insufficient, CPFE is under-recognized. Male patient presented with progressive dyspnea and history of smoking 60 packs per year. Upper lobe emphysema and lower lobe fibrosis, which are specific for CPFE syndrome, were observed in chest computed tomography scans. Forced expiratory volume 1 was relatively well preserved, but diffusing capacity of the lungs for carbon monoxide was very low, and is an important feature of the disease. Pulmonary hypertension has also been determined to be characteristic finding of the syndrome. Patient was diagnosed as CPFE syndrome based on presence of all characteristic features and case is presented with review of the literature to draw attention to this disease.

Keywords: emphysema, fibrosis, pulmonary hypertension

Dildar Duman, Hakan Gnen. A new definition: Combined pulmonary fibrosis and emphysema syndrome. Respir Case Rep. 2017; 6(2): 110-113

Sorumlu Yazar: Dildar Duman, Trkiye
Makale Dili: Trke
LookUs & Online Makale