Konjenital Pulmoner Havayolu Malformasyonu Zemininde Geli�en Mezenkimal T�m�r Ol-gusu

K�l��, Tar�k; I��k, �ehmus; Selimo�lu �en, Hadice

Cilt : 13 Say� : 1 Y�l : 2024

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Konjenital Pulmoner Havayolu Malformasyonu Zemininde Geli�en Mezenkimal T�m�r Ol-gusu [Respir Case Rep]

Respir Case Rep. 2024; 13(1): 58-61 | DOI: 10.5505/respircase.2024.24482

Konjenital Pulmoner Havayolu Malformasyonu Zemininde Geli�en Mezenkimal T�m�r Ol-gusu

Tar�k K�l��, �ehmus I��k, Hadice Selimo�lu �en
Dicle �niversitesi T�p Fak�ltesi, G��s Hastal�klar� Ana Bilim Dal�, Diyarbak�r

Konjenital pulmoner havayolu malformasyonu nadir g�r�len ve akci�erin geli�imsel bir anomalisidir. Stocker taraf�ndan s�n�fland�r�lm�� olup be� tipe ayr�lm��t�r. Genellikle, prenatal rutin ultrasonografi sayesinde tan� bu d�nemde konur. Ancak baz� olgular asemptomatik seyretti�i i�in ileri ya�a kadar tan� almayabilir. Klinik olarak, nefes darl��, siyanoz ve yenido�an d�neminde respiratuar distress ile prezente olabilir. �leri ya�ta tekrarlayan enfeksiyonlar�n nedeni olabilir. Malign transformasyon literat�rde tan�mlanm�� bir antitedir. Olgumuz hem ileri ya�ta tan� alm�� olmas� hem de mezenkimal t�m�r geli�imi nedeniyle literat�re katk� sa�lamak i�in sunuldu.

Anahtar Kelimeler: Konjenital Pulmoner Havayolu Malformasyonu, Mezenkimal T�m�r, Bronkopulmoner Sekestrasyon.

A Case of Mesenchymal Tumor Developing on the Background of Congenital Pulmonary Airway Malformation

Tar�k K�l��, �ehmus I��k, Hadice Selimo�lu �en
Department of Pulmonary Diseases, Faculty of Medicine, Dicle University, Diyarbak�r, T�rkiye

Congenital pulmonary airway malformations are rare developmental lung anomalies, five types of which have been classified by Stocker. The condition is generally diagnosed prenatally during routine prenatal ultrasonography, however, some cases are asymptomatic and so may not be diagnosed until later in life. Clinically, the condition can present in newborns with shortness of breath, cyanosis and respiratory distress, and may lead to recurrent infections in later ages, and malignant transformations have been defined in literature. Here, we present a case that may be of interest to literature not only due to the diagnosis later in life, but also due to the development of a mesenchymal tumor in the background.

Keywords: Congenital pulmonary airway malformation, Me-senchymal Tumor, Bronchopulmonary Sequestration.

Sorumlu Yazar: Tar�k K�l��, T�rkiye
Makale Dili: �ngilizce

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