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Laparoscopic Endoscopic Surgical Science Bronektazili Bir Hastada Gecikmi Tan: Swyer-James-MacLeod Sendromu [Respir Case Rep]
Respir Case Rep. 2013; 2(1): 39-43 | DOI: 10.5505/respircase.2013.14622

Bronektazili Bir Hastada Gecikmi Tan: Swyer-James-MacLeod Sendromu

Dilay Ahat imen, Aydanur Ekici, Emel Bulcun, Mehmet Ekici
1. Krkkale niversitesi, Tp Fakltesi, Gs Hastalklar Blm, Krkkale, Trkiye

Swyer-James/Mac Leod Sendromu (SJMS) pulmoner arter hipoplazisine bal unilateral hiperlsent akcier grnm ve bronektazi ile karakterize nadir grlen bir hastalktr. ocukluk anda geirilen viral broniolit ve pnmoniler sonras akkiz olarak gelitii dnlmektedir. Krk sekiz yanda kadn hasta, nefes darl, ksrk, balgam karma yaknmalaryla bavurdu. yksnden bu ikayetlerinin ocukluk yalarndan beri tekrarlad, 10 yl ncesine kadar kronik bronit, son 10 yldr da bronektazi ve kk hava yolu hastal tanlaryla takip ve tedavi edildii renildi. Fizik muayenesinde; solunum seslerinin iddeti sa alt blgede sola gre azalm, bilateral orta ve alt blgede ve anteriorda kaba ralleri mevcuttu. Akcier grafisinde; sol akcierde hacim kayb, radyolusensi art ve alt zonda bronektazik alanlar izlendi. Bilgisayarl tomografide; sol pulmoner arter ve dallarnn kalibrasyonu saa kyasla belirgin azalmt. SJMS ocukluk ve gen erikin dnemde tehis edilen bir hastalk olmasna karn, olgumuzda 48 yana kadar solunum ikayetleri tanmlamas nedeniyle birok kez tetkikler yaplmasna ramen tan konulmamtr. Tek tarafl hiperlsent akcier grnm saptandnda bu sendromun ayrc tanda dnlmesi gerektiini vurgulamak iin sunuyoruz.

Anahtar Kelimeler: Bronektazi, Hiperlsent akcier, Swyer-James /Macleod Sendromu.

Delayed Diagnosis in a Patient with Bronchiectasis: Swyer-James-MacLeod Syndrome

Dilay Ahat imen, Aydanur Ekici, Emel Bulcun, Mehmet Ekici
Kirikkale University, Faculty Of Medicine, Department Of Pulmonary Medicine, Kirikkale, Turkey

Swyer-James/MacLeod syndrome (SJMS) is a rare disease, characterized by unilateral hyperlucent lung due to hypoplasia of the pulmonary artery and bronchiectasis. Illnesses such as viral bronchiolitis and pneumonia in childhood are thought to be an acquired form. A 48-year-old woman applied to the hospital with symptoms including shortness of breath, sputum, and cough. Her medical history revealed that these symptoms had been relapsing since her childhood. She had been diagnosed and monitored for chronic bronchitis and bronchiectasis for the past 10 years. A physical examination revealed that the respiratory sounds of the lower left lobe decreased more than the right side, and revealed coarse crackles in the both middle, anterior, and inferior hemithorax. Chest radiography showed a loss of volume of the left lung, hiperlucency, and areas of bronchiectasis in the lower left lobe. Computed tomography showed that calibration of left pulmonary artery and its branches significantly decreased compared to the right side. We present our case simply because the majority of SJMS cases are diagnosed in childhood and young adulthood; however, our patient was examined several times with the same symptoms and not diagnosed until the age of 48. This syndrome should be considered in the differential diagnosis of patients who have hyperlucent lung.

Keywords: Bronchiectasis, Hyperlucent lung, Swyer-James /Macleod Syndrome.

Dilay Ahat imen, Aydanur Ekici, Emel Bulcun, Mehmet Ekici. Delayed Diagnosis in a Patient with Bronchiectasis: Swyer-James-MacLeod Syndrome. Respir Case Rep. 2013; 2(1): 39-43

Sorumlu Yazar: Dilay Ahat imen, Trkiye
Makale Dili: Trke
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